Tsis Meej Pem Nrog Cushing's Disease
Tsis Meej Pem Nrog Cushing's Disease

Video: Tsis Meej Pem Nrog Cushing's Disease

Video: Tsis Meej Pem Nrog Cushing's Disease
Video: The Voices of Cushing’s Disease, Part I: Living with the Reality 2024, Tej zaum
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Lub lim tiam dhau los, MiamiAngel tau thov kom kuv coj Cushing's disease, lossis hyperadrenocorticism raws li nws tau hu. Kuv zoo siab yuav tsum.

Raws li MiamiAngel hmoov tsis pom pom, kev kuaj mob Cushing's disease tsis yooj yim. Ua ntej tshaj, cov tsos mob tuaj yeem ua rau me ntsis thiab pom nrog lwm cov kab mob tib yam. Cov cim ntawm Cushing's disease yog:

  • Muaj ntau yam qab los noj mov
  • Nce nqhis dej thiab tso zis
  • Lub tsho tiv no tsis zoo
  • Cov teeb meem ntawm daim tawv nqaij
  • Cov kab mob kis
  • Rau nkawv
  • Nqaij tsis muaj zog
  • Lub lauj kaub-bellied tsos
  • Neurologic pauv hloov pauv nyob rau qib siab pituitary-hyperadrenocorticism

Nco ntsoov tias txhua tus dev Cushingoid tsis tas yuav muaj tag nrho cov tsos mob no.

Qhov pib ua rau Cushing's yog kev ua haujlwm ntau dhau ntawm hormone cortisol lossis kev siv tshuaj ntau ntau los ntawm corticosteroid zoo li prednisone. Feem ntau cortisol hauv lub cev yog tsim los ntawm cov qog adrenal. Yog tias qog cov qog ntawm cov qog, nws tuaj yeem kho cov tshuaj hormones ntau dua. Cov qog adrenal yog lub luag haujlwm rau kwv yees li 20 feem pua ntawm Cushing tus mob hauv cov dev, feem ntau ua rau cov tsiaj loj.

Mob qog hauv lub qog pituitary, nyob hauv lub hlwb, kuj tseem tuaj yeem ua rau cov qog adrenal ua haujlwm ntau dua li cortisol dua li ib txwm muaj. Cov qog Pituitary ua lub luag haujlwm yog li ntawm 80 feem pua ntawm cov neeg mob Cushing's mob.

Kuv lis kuaj xyuas Cushing's disease thaum kuv muaj tus neeg mob uas tau ua tej yam txawv txawv li no:

1. Khiav lub chaw tso tshuaj lom neeg ntshav, ua kom tiav cov ntshav ntawm tes, tso zis, thiab lwm yam haujlwm (piv txwv li, kuaj mob plawv lossis kuaj quav) uas yuav raug hu raws li dev lub cev kev kuaj mob thiab keeb kwm. Cov txiaj ntsig yuav tsum yog taw rau mus rau (piv txwv li, txhawb cov qib phosphatase alkaline thiab kev nyuaj siab leukogram) lossis deb ntawm Cushing's.

2. Kuv tseg ib qhov hnoos qeev rau cortisol: kev tshuaj ntsuam tus kab mob creatinine. Yog tias cov txiaj ntsig tsis tau zoo, Cushing's disease yog qhov tsis tshua muaj tshwm sim. Yog tias lawv nce siab, Cushing's disease muaj peev xwm ua tau, tab sis tsis muaj kev kuaj pom tseeb, vim tias lwm yam kab mob tuaj yeem ua rau tib yam tshwm sim.

3. Txheeb xyuas feem ntau (tab sis tsis yog txhua txhua) ntawm Cushing's disease thiab txiav txim siab tias daim ntawv pituitary lossis adrenal ntawm tus kab mob no yog qhov twg (uas yog qhov tseem ceeb rau kev xaiv txoj kev kho mob) yog ua tau nrog qee qhov sib xyaw ua ke ntawm ACTH kev sim, qis qis koob tshuaj dexamethasone rau kev tshuaj xyuas kev noj qab haus huv, kev txhaj tshuaj dexamethasone ntau dua, thiab / lossis ultrasound ntsuas plab. Cov kev ntsuam xyuas twg kuv khiav ua qhov kev txiav txim twg yog ua raws li tus dev qhia thiab seb tus tswv xav tau qhov kev kuaj mob sai thiab ua tiav lossis xav tau qhov kev qhia ua ntu zus thiab muaj feem yuav zam rau kev siv nyiaj uas tsis tsim nyog.

Peb muaj cov kev xaiv thaum nws los txog rau kev kho mob ntawm Cushing's disease. Yog tias cov tsos mob ntawm tus dev tsis loj heev, (piv txwv li, nws tau ua panting ntau dua tab sis muaj qhov txawv txav), kev kho yuav tsis tuaj yeem lav tshwj tsis yog cov teeb meem tsis zoo nyob rau lub sijhawm. Daim ntawv pituitary ntawm tus kab mob feem ntau yog kho nrog mitotane lossis trilostane, ob qho tib si ntawm kev tua cortisol ntau lawm. Cov tshuaj selegeline kuj tseem tuaj yeem siv los tswj cov tsos mob cuam tshuam nrog Cushing's tab sis nws tsis zoo li mitotane lossis trilostane. Cov qog uas tsis yog-cov neeg mob tau zoo tshaj yog kev phais. Yog hais tias kev phais mob tsis yog ib qho kev xaiv, cov lus tau hais los saud muaj qee cov txiaj ntsig rau adrenal daim ntawv ntawm tus kabmob.

Yuav tsum saib xyuas cov dev raws li kev kho kom Cushing's yog qhov tseem ceeb. Peb lub hom phiaj yog txhawm rau txhawm rau tua cortisol ntau txaus kom cov tsiaj muaj kev noj qab haus huv, tab sis tsis yog li ntawd peb tsim qhov teeb meem rov qab - hypoadrenocorticism, lossis Addison's disease.

Cov dev nrog Cushing tus kab mob tuaj yeem xav tias yuav nyob peb xyoos, lossis ntev dua, tom qab kuaj mob nrog kev kho mob uas tsim nyog thiab muaj hmoo me ntsis, tab sis nws yuav tsum nco ntsoov tias thaum qhov xwm txheej no feem ntau tuaj yeem tswj tau zoo, nws tsuas yog tsawg kho tau.

Duab
Duab

Dr. Jennifer Coates

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