Cov txheej txheem:

Myelin Deficiency Hauv Miv
Myelin Deficiency Hauv Miv

Video: Myelin Deficiency Hauv Miv

Video: Myelin Deficiency Hauv Miv
Video: Myelin (Dub) 2024, Kaum ib hlis
Anonim

Hypomyelination hauv miv

Cov khoom siv roj ntsha uas npog cov axons (ntu ntawm cov hlab hlwb uas hloov impulses mus rau lwm lub hlwb ntawm lub cev), myelin ua haujlwm pabcuam tseem ceeb rau cov kabmob ntawm lub paj hlwb: raws li lub rwb thaiv tsev, tiv thaiv cov hlab ntsha los ntawm sab nraud cuam tshuam, thiab raws li kev pabcuam rau kev xa mus tom ntej cov txheej txheem ntawm cellular kis ntawm cov hlab hlwb cov kev ua. Yog li no, hypomyelination, lossis kev tsim tawm tsis txaus ntawm myelin hauv lub cev, tuaj yeem ua rau mob rau lub hauv nruab nrab cov hlab ntsha (CNS). Nws tuaj yeem ua rau tshee tshee, uas yog qhov pom tseeb thaum tus miv yog nquag.

CNS hypomyelination muaj kev paub ntau dua ntawm kev kuaj mob hauv kab mob Siamese.

Cov tsos mob

Cov leeg hauv nruab nrab:

  • Cov chaw kuaj mob tshwm nyob rau hauv hnub yug
  • Lub cev tshee uas cuam tshuam nrog kev ua si thiab poob thaum lub sijhawm so
  • Cov tsos mob feem ntau txhim kho los ntawm ib xyoos

Hlov Puag Ncig Zog:

  • Clinical cov cim tshwm sim thaum 5-7 lub lim tiam ntawm lub hnub nyoog
  • Neeg tsis muaj zog
  • Incoordination ntawm nraub qaum (ataxia)
  • Nqaij plua plav
  • Cov Hyporeflexia (qis dua qhov qub lossis tsis mob)
  • Cov tsos mob tsis daws nrog lub hnub nyoog

Ua rau

  • Qhov tsis paub yog vim li cas, tab sis kab mob kis los yog lom yog xam, tshwj xeeb tshaj yog vim cov tsos mob feem ntau daws
  • Tus kab mob paj hlwb peripheral keeb kwm tsis paub txiav txim, tab sis xav tias yog txhob kaw

Kev kuaj mob

Tus kws kho tsiaj yuav ua ib qho kev kuaj mob thoob plaws koj lub miv, suav txog keeb kwm yav dhau los ntawm cov tsos mob thiab koj tus keeb kwm keeb kwm keeb kwm. Cov kev ntsuas ntshav muaj xws li kuaj cov ntshav, suav nrog cov ntshav qhia tshuaj, suav cov ntshav ua tiav, thiab urinalysis.

Kev kuaj mob yog ua raws li cov kev tshawb fawb pom tias koj tus miv tab tom nthuav tawm, tab sis rau kev txheeb xyuas meej meej, koj tus kws kho tsiaj yuav nqa ib qho qauv / kev kuaj mob ntawm lub paj hlwb mus soj ntsuam kom txaus myelin ntawm txoj hlab ntaws. Koj tus kws kho mob tej zaum yuav xaiv los ua lub hlwb mus kuaj. Lwm yam kev qhia suav nrog electromyography, uas ntsuas qhov hluav taws xob kev ua thiab lub peev xwm ntawm cov leeg mob. Hauv qhov xwm txheej no, kev tshawb pom feem ntau tsis muaj dab tsi tshwm sim me me. Lub cev muaj zog ntawm cov hluav taws xob sib xyaw ua ke tuaj yeem siv los ntsuas qhov muaj peev xwm ntawm lub cev muaj zog thiab siv hluav taws xob kom hnov hluav taws xob. Nrog hypomyelination, feem ntau maj mam conduction lossis tsuas yog me me ntawm qhov muaj peev xwm.

Kev Kho Mob

Tsis muaj ib txoj kev kho tau zoo rau kev kho mob ib leeg lossis nruab nrab hypomyelination.

Nyob thiab Tswj

Vim tias caj ces muaj raws caj ces ntawm tus kabmob no, yog tias koj tus miv raug kuaj mob nrog tus kabmob no, koj yuav tau qhia kom tsis txhob yug koj tus miv, lossis yug menyuam ntxiv tus niam txiv ntawm tus menyuam kis mob. Yog tias koj tus miv raug cuam tshuam los ntawm CNS hypomyelination, cov tsos mob tshee yuav feem ntau txhim kho kuv lub sijhawm koj tus miv nce mus txog thawj xyoo uas muaj hnub nyoog. Nrog PNS hypomyelination, cov miv cuam tshuam yuav tsum muaj lub cev tiag tiag.

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